Gibbus deformity is a form of structural kyphosis typically found in the upper lumbar and lower thoracic vertebrae, where one or more adjacent vertebrae become wedged. Gibbus deformity most often develops in young children as a result of spinal tuberculosis and is the result of collapse of vertebral bodies.[1][2][3] This can in turn lead to spinal cord compression causing paraplegia.[4][5]
Gibbus deformity in a chest X-ray (frontal and lateral) of an old woman.
In addition to tuberculosis, other possible causes of gibbus deformity include pathological diseases, hereditary and congenital conditions, and physical trauma to the spine that results in injury.[6][7] Gibbus deformity may result from the sail vertebrae associated with cretinism (the childhood form of hypothyroidism), mucopolysaccharidosis (MPS), and certain congenital syndromes, including achondroplasia.[8] Because most children with MPS I (Hurler Syndrome) also exhibit symptoms of a gibbus deformity, the latter can possibly be used to identify the former.[9]
Gibbus deformity is included in a subset of structural kyphosis that is distinguished by a higher-degree angle in the spinal curve that is specific to these forms of kyphosis. Other conditions within this subset include Pott's disease and Scheuermann kyphosis, but gibbus deformity is marked by an especially sharp angle. Viewed from behind, the resulting hunchback is more easily seen when bending forward.[10] A kyphosis of >70° can be an indication of the need for surgery and these surgeries can be necessary for children as young as two years old, with a reported average of 8 years of age.[9]
Referencesedit
^Kasper D.L. et al., Harrisons principles of internal medicine, 16.ed, 2005 p.958
^Batirel, A.; Erdem, H.; Sengoz, G.; Pehlivanoglu, F.; Ramosaco, E.; Gülsün, S.; Tekin, R.; Mete, B.; Balkan, İ.İ. (2015). "The course of spinal tuberculosis (Pott disease): results of the multinational, multicentre Backbone-2 study". Clinical Microbiology and Infection. 21 (11): 1008.e9–1008.e18. doi:10.1016/j.cmi.2015.07.013. PMID 26232534.
^Garg, Ravindra Kumar; Somvanshi, Dilip Singh (2011-09-01). "Spinal tuberculosis: A review". The Journal of Spinal Cord Medicine. 34 (5): 440–454. doi:10.1179/2045772311y.0000000023. ISSN 1079-0268. PMC3184481. PMID 22118251.
^Davidson's Principles and Practice of Medicine, 20th Ed, 2006.
^Ghandi, Mehak; Aycock, Ryan D.; Berwald, Nicole; Hahn, Barry (2015). "Gibbus Deformity". The Journal of Emergency Medicine. 49 (3): 340–341. doi:10.1016/j.jemermed.2015.04.004. PMID 26095218.
^Yaman, Onur; Dalbayrak, Sedat (2013). "Kyphosis and review of the literature". Turkish Neurosurgery. 24 (4): 455–65. doi:10.5137/1019-5149.jtn.8940-13.0. ISSN 1019-5149. PMID 25050667.
gibbus, deformity, form, structural, kyphosis, typically, found, upper, lumbar, lower, thoracic, vertebrae, where, more, adjacent, vertebrae, become, wedged, most, often, develops, young, children, result, spinal, tuberculosis, result, collapse, vertebral, bod. Gibbus deformity is a form of structural kyphosis typically found in the upper lumbar and lower thoracic vertebrae where one or more adjacent vertebrae become wedged Gibbus deformity most often develops in young children as a result of spinal tuberculosis and is the result of collapse of vertebral bodies 1 2 3 This can in turn lead to spinal cord compression causing paraplegia 4 5 Gibbus deformity in a chest X ray frontal and lateral of an old woman In addition to tuberculosis other possible causes of gibbus deformity include pathological diseases hereditary and congenital conditions and physical trauma to the spine that results in injury 6 7 Gibbus deformity may result from the sail vertebrae associated with cretinism the childhood form of hypothyroidism mucopolysaccharidosis MPS and certain congenital syndromes including achondroplasia 8 Because most children with MPS I Hurler Syndrome also exhibit symptoms of a gibbus deformity the latter can possibly be used to identify the former 9 Gibbus deformity is included in a subset of structural kyphosis that is distinguished by a higher degree angle in the spinal curve that is specific to these forms of kyphosis Other conditions within this subset include Pott s disease and Scheuermann kyphosis but gibbus deformity is marked by an especially sharp angle Viewed from behind the resulting hunchback is more easily seen when bending forward 10 A kyphosis of gt 70 can be an indication of the need for surgery and these surgeries can be necessary for children as young as two years old with a reported average of 8 years of age 9 References edit Kasper D L et al Harrisons principles of internal medicine 16 ed 2005 p 958 Batirel A Erdem H Sengoz G Pehlivanoglu F Ramosaco E Gulsun S Tekin R Mete B Balkan I I 2015 The course of spinal tuberculosis Pott disease results of the multinational multicentre Backbone 2 study Clinical Microbiology and Infection 21 11 1008 e9 1008 e18 doi 10 1016 j cmi 2015 07 013 PMID 26232534 Garg Ravindra Kumar Somvanshi Dilip Singh 2011 09 01 Spinal tuberculosis A review The Journal of Spinal Cord Medicine 34 5 440 454 doi 10 1179 2045772311y 0000000023 ISSN 1079 0268 PMC 3184481 PMID 22118251 Davidson s Principles and Practice of Medicine 20th Ed 2006 Ghandi Mehak Aycock Ryan D Berwald Nicole Hahn Barry 2015 Gibbus Deformity The Journal of Emergency Medicine 49 3 340 341 doi 10 1016 j jemermed 2015 04 004 PMID 26095218 Yaman Onur Dalbayrak Sedat 2013 Kyphosis and review of the literature Turkish Neurosurgery 24 4 455 65 doi 10 5137 1019 5149 jtn 8940 13 0 ISSN 1019 5149 PMID 25050667 Castriota Scanderbeg Alessandro 2005 Spine Abnormal Skeletal Phenotypes Springer Berlin Heidelberg pp 167 232 doi 10 1007 3 540 30361 8 3 ISBN 978 3540303619 Hecht Jacqueline T Butler Ian J 1990 Neurologic Morbidity Associated With Achondroplasia Journal of Child Neurology 5 2 84 97 doi 10 1177 088307389000500203 PMID 2161033 S2CID 19737483 a b White K K 2011 12 01 Orthopaedic aspects of mucopolysaccharidoses Rheumatology 50 suppl 5 v26 v33 doi 10 1093 rheumatology ker393 ISSN 1462 0324 PMID 22210667 Kyphosis Description and Diagnosis SpineUniverse Retrieved 2017 11 15 nbsp This human musculoskeletal system article is a stub You can help Wikipedia by expanding it vte Retrieved from https en wikipedia org w index php title Gibbus deformity amp oldid 1081632191, wikipedia, wiki, book, books, library,
